Pulmonary microcystic fibromyxoma: a rare benign myxoid tumor in the lung
نویسندگان
چکیده
Primary pulmonary microcystic fibromyxoma is very rare. We describe a case of 68-year-old female who had a 4 months history of thorax suffocation and dyspnea. Computed tomography revealed a well-circumscribed nodule with a diameter of approximately 2.2 cm in the right upper lobe. After extensive workup, she received a right upper lobe wedge resection. Pathologically, microcystic architecture with myxoid stroma was revealed in the wellcircumscribed tumor. The tumor cells were spindled to stellate, with innocuous appearance. Immunohistochemical staining showed strong expression of vimentin and CD99 in the tumor cells, but no expression of epithelial markers and other mesenchymal markers for distinctive differentiation. Genetically no EWSR1 or SS18 rearrangements were detected by fluorescence in situ hybridization. Eventually this case was diagnosed as primary pulmonary microcystic fibromyxoma. No tumor recurrence or metastasis was observed during 25 months follow-up.
منابع مشابه
Fibromyxoma of the axis.
Fibromyxoma of bone is a rare benign tumor of fibrous tissue origin. The typical location is the jaws. Sporadic extragnathic cases have been reported, but fibromyxoma of the spine has not been reported. The histological appearance of fibromyxoma is benign and includes abundant extracellular fibrous and myxoid stroma with varying amounts of calcification and ossification. Myxoid changes are usua...
متن کاملSuperficial Acral Fibromyxoma: a Rare Tumor Diagnosed by Cytology
Superficial acral fibromyxoma are rare soft tissue tumors predominantly involving hands and feet of adults. There are only a few reported cases of this benign neoplasm, but no FNAC diagnosis of this tumor is reported in the literature. A Forty-eight year old female presented with a 5 x 3.5 cm globular, firm swelling over the right fifth toe. Fine needle aspiration cytology (FNAC) of the lesion...
متن کاملMicrocystic Adnexal Carcinoma of Posterior Neck: A Case Report
Background: Microcystic adnexal tumor is a rare sclerosing variant of ductal carcinoma of eccrine sweat glands which is highly invasive. This tumor is often misdiagnosed as other benign or malignant skin lesions and improper treatment is carried on and is associated with high recurrence rate. Case presen...
متن کاملPlexiform Fibromyxoma: A Rare Gastric Tumor
Plexiform fibromyxoma is a rare and distinctive benign mesenchymal neoplasm that occurs in the gastric antrum. This tumor has a potential for misdiagnosis as gastrointestinal stromal tumor (GIST). It causes mucosa and vascular ulcerations without advancement of the tumor. Cytological bland spindle cells within a variably myxoid stroma characterize the histology of the tumor. We report the case ...
متن کاملA case of recurrent superficial acral fibromyxoma.
Superficial acral fibromyxoma (SAFM) is a rare myxoid tumor that was first described in 2001. The presence of a very slow growing solitary tender mass in the subungual area is the typical clinical feature at presentation. Histopathologically, SAFM is composed of stellate cells in a myxocollagenous matrix with a poorly circumscribed margin. This tumor is thought to be benign, but its natural cou...
متن کامل